Dermatology Made Easy is based on the most popular topics from DermNet NZ's vast array of material. The book combines the essential focus of the ‘Made Easy’ book series with the authority and knowledge base of DermNet NZ's unparalleled resources.
Author: Brian Wu PhD. MD Candidate, Keck School of Medicine, Los Angeles, USA; Chief Editor: Hon A/Prof Amanda Oakley, Dermatologist, Hamilton, New Zealand, February 2016.
Adams-Oliver syndrome is a rare condition characterised by various malformations of the limbs and abnormal skin development, particularly on the scalp.
Adams-Oliver syndrome is also known as:
Adams-Oliver syndrome is considered to be very rare, with an incidence of about 1 in 225,000 live births. The aetiology is unknown. However:
Adams-Oliver syndrome is caused by genetic mutations in at least 6 genes:
The primary features of Adams-Oliver syndrome include:
Diagnosis is based on clinical signs and symptoms, patient/family history and imaging.
There is no cure for Adams-Oliver syndrome; treatment focuses in on symptom management and can include:
Long-term prognosis for Adams-Oliver syndrome is difficult to predict: it is not adequately described in medical literature due to a dearth of cases.
It should be noted that, in absence of major abnormalities, those with this condition should have a normal lifespan.
© 2018 DermNet New Zealand Trust.
DermNet NZ does not provide an online consultation service. If you have any concerns with your skin or its treatment, see a dermatologist for advice.